Mouse Anti-GAA Antibody (CBMOAB-43281FYA)
Cat: CBMOAB-43281FYA
Certificate of Analysis Lookup
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Lot Number
To download a Certificate of Analysis, please enter a lot number in the search box below. Note: Certificate of Analysis not available for kit components.
Lot Number
- Product List
- Specifications
- Application Information
- Target
| Sub Cat | Clonality | Species Reactivity | Application | Clone | Conjugate | Size | |
| CBMOAB-43281FYA | Monoclonal | Rhesus (Macaca mulatta), Cattle (Bos taurus), Chimpanzee (Pan troglodytes), Pig (Sus scrofa), Zebrafish (Danio rerio) | WB, ELISA | MO43281FYA | 100 µg | ||
| CBMOAB-77377FYA | Monoclonal | Zebrafish (Danio rerio) | WB, ELISA | MO77377FYA | 100 µg | ||
| MO-AB-12803R | Monoclonal | Cattle (Bos taurus) | WB, ELISA | MO12803R | 100 µg | ||
| MO-AB-18548W | Monoclonal | Chimpanzee (Pan troglodytes) | WB, ELISA | MO18548W | 100 µg | ||
| MO-AB-25974R | Monoclonal | Pig (Sus scrofa) | WB, ELISA | MO25974R | 100 µg |
Specifications
| Host species | Mouse (Mus musculus) |
| Species Reactivity | Rhesus (Macaca mulatta), Cattle (Bos taurus), Chimpanzee (Pan troglodytes), Pig (Sus scrofa), Zebrafish (Danio rerio) |
| Clone | MO43281FYA |
| Specificity | This antibody binds to Rhesus GAA. |
| Format | Liquid or Lyophilized |
| Storage | Store at 4°C: short-term (1-2weeks) Store at -20°C: long-term and future use |
| Purity | > 90% was determined by SDS-PAGE |
| Purification | Purified with Protein A or G affinity chromatography |
Application Information
| Application | WB, ELISA |
| Application Notes | ELISA: 1:1000-1:3000 Other applications are to be developed. The optimal dilution should be determined by the end user. |
Target
| Introduction | This gene encodes lysosomal alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. The encoded preproprotein is proteolytically processed to generate multiple intermediate forms and the mature form of the enzyme. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Alternative splicing results in multiple transcript variants. |
| Product Overview | Mouse Anti-Rhesus GAA Antibody is a mouse antibody against GAA. It can be used for GAA detection in Western Blot, Enzyme-Linked Immunosorbent Assay. |
| Alternative Names | Lysosomal alpha-glucosidase preproprotein; GAA |
| UniProt ID | H9EXA2 |
| Protein Refseq | The length of the protein is 952 amino acids long. The sequence is show below: MGVRHPLCSRRLLAVCALVSLATAVLLGHILLHDFLLVPRELSGSSSVLEETRPARQQGASRPGPQNAQAHPGCPRAVPTQCDVPPNSRFDCAPDKAITQEQCEARGCCYIPAKQELRRAQMGQPWCFFPPSYPSYKLENLSASEMGYTATLTRTTPTFFPKDILTLRLDVMMETENRLHFTIKDPANKRYEVPLETPRVPSRALSPLYSVEFSEEPFGVIVRRQLDGRVLLNTTVAPLFFADQFLQLSTSLPSQYITGLAEHLSPLMLSTSWTRITLWNRDLAPTPGANLYGSHPFYLALEDGGSAHGVFLLNSNAMDVVLQPSPALSWRSTGGILDVYIFLGPEPKSVVRQYLDVVGYPFMPPYWGLGFHLCRWGYSSTAITRQVVENMTRAHFPLDVQWNDLDYMDSRRDFTFNKDGFRDFPAMVQELHQGGRRYVMIVDPAISSSGPAGSYRPYDEGLRRAVFITNETGQPLIGKVWPGSTAFPDFTNPAALAWWEDMVAEFHDQVPFDGMWIDMNEPSNFIRGSEDGCPHNELEEPPYVPGVVGGTLQAATICASSHQFLSTHYNLHNLYGLTEAIASYRALVKARGTRPFVISRSTFAGHGRYAGHWTGDVWSSWEQLAASVPEILQFNLLGVPLVGADVCGFLGNTSEELCVRWTQLGAFYPFMRNHNGLLNLPQEPYSFSEPAQQAMRKALTLRYALLPHLYTLFHQAHVAGETVARPLFLEFPEDSSTWTVDHQLLWGEALLITPVLQAGKAEVTGYFPSGTWYDLETVPIEALGSLPPPPAAPREPAIHSEGQWVTLPAPLDTINVHLRAGHIIPLQGPGLTTTESRQQPMALAVALTKGGEARGELFWDDGESLEVLERGAYTQVIFLARSNTVMNELVHVTSEGAGLQLQKVTVLGVATAPQQVLSNGAPVSNFTYSPDTKVLDIPVSLLVGEQFLISWS. |
For Research Use Only | Not For Clinical Use.
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