Adenylosuccinate lyase
The protein encoded by this gene belongs to the lyase 1 family. It is an essential enzyme involved in purine metabolism, and catalyzes two non-sequential reactions in the de novo purine biosynthetic pathway: the conversion of succinylaminoimidazole carboxamide ribotide (SAICAR) to aminoimidazole carboxamide ribotide (AICAR) and the conversion of adenylosuccinate (S-AMP) to adenosine monophosphate (AMP). Mutations in this gene are associated with adenylosuccinase deficiency (ADSLD), a disorder marked with psychomotor retardation, epilepsy or autistic features. Alternatively spliced transcript variants have been found for this gene.
Mouse Anti-ADSL Antibody (MO-AB-06265Y) (CAT#: MO-AB-06265Y)
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- Host species: Mouse
- Species Reactivity: O. anatinus (Ornithorhynchus anatinus), Cattle (Bos taurus), Chicken (Gallus gallus), Chimpanzee (Pan troglodytes), Elephant (Loxodonta africana), Ferret (Mustela Putorius Furo), Frog (Xenopus laevis), Fruit fly (Drosophila melanogaster), Guinea pig (Cavia porcellus), Hamsters (Cricetinae), Horse (Equus caballus), Malaria parasite, Mallard (Anas platyrhynchos), Pig (Sus scrofa), Rabbit (Oryctolagus cuniculus), Rhesus (Macaca mulatta), Sheep (Ovis aries), Zebrafish (Danio rerio)
- Application: WB, ELISA
- Protein: Adenylosuccinate lyase
- Size: 0.5mg, 1mg, 200µg
- Conjugate: AP, APC, Biotin, Consult us more, Cy3, Cy5, Cy5.5, Cy7, FITC, HRP, NONE, PE, PerCP
- Alternative Names: Adenylosuccinate lyase, ASL, EC 4.3.2.2, Adenylosuccinase, ADSL
Mouse Anti-ADSL Antibody (MO-AB-50533W) (CAT#: MO-AB-50533W)
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- Host species: Mouse
- Species Reactivity: Marmoset, Cattle (Bos taurus), Chicken (Gallus gallus), Chimpanzee (Pan troglodytes), Elephant (Loxodonta africana), Ferret (Mustela Putorius Furo), Frog (Xenopus laevis), Fruit fly (Drosophila melanogaster), Guinea pig (Cavia porcellus), Hamsters (Cricetinae), Horse (Equus caballus), Malaria parasite, Mallard (Anas platyrhynchos), Pig (Sus scrofa), Rabbit (Oryctolagus cuniculus), Rhesus (Macaca mulatta), Sheep (Ovis aries), Zebrafish (Danio rerio)
- Application: WB, ELISA
- Protein: Adenylosuccinate lyase
- Size: 0.5mg, 1mg, 200µg
- Conjugate: AP, APC, Biotin, Consult us more, Cy3, Cy5, Cy5.5, Cy7, FITC, HRP, NONE, PE, PerCP
- Alternative Names: Adenylosuccinate lyase, ASL, EC 4.3.2.2, Adenylosuccinase, ADSL
For Research Use Only | Not For Clinical Use.