Mouse Anti-Frog abca4 Antibody (MO-AB-01126H)
Cat: MO-AB-01126H
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- Product Details
Specifications
Host species | Mouse (Mus musculus) |
Species Reactivity | Frog (Xenopus laevis) |
Clone | MO01126C |
Specificity | This antibody binds to Frog abca4. |
Format | Liquid or Lyophilized |
Storage | Store at 4°C: short-term (1-2weeks) Store at -20°C: long-term and future use |
Purity | > 90% was determined by SDS-PAGE |
Purification | Purified with Protein A or G affinity chromatography |
Application Information
Application | WB, ELISA |
Application Notes | ELISA: 1:1000-1:3000 Other applications are to be developed. The optimal dilution should be determined by the end user. |
Target
Introduction | The membrane-associated protein encoded by this gene is a member of the superfamily of ATP-binding cassette (ABC) transporters. ABC proteins transport various molecules across extra- and intracellular membranes. ABC genes are divided into seven distinct subfamilies (ABC1, MDR/TAP, MRP, ALD, OABP, GCN20, White). This protein is a member of the ABC1 subfamily. Members of the ABC1 subfamily comprise the only major ABC subfamily found exclusively in multicellular eukaryotes. This protein is a retina-specific ABC transporter with N-retinylidene-PE as a substrate. It is expressed exclusively in retina photoreceptor cells, indicating the gene product mediates transport of an essental molecule across the photoreceptor cell membrane. Mutations in this gene are found in patients diagnosed with Stargardt disease, a form of juvenile-onset macular degeneration. Mutations in this gene are also associated with retinitis pigmentosa-19, cone-rod dystrophy type 3, early-onset severe retinal dystrophy, fundus flavimaculatus, and macular degeneration age-related 2. |
Product Overview | This product is a mouse antibody against abca4. It can be used for abca4 detection in Western Blot, Enzyme-Linked Immunosorbent Assay. |
Alternative Names | Retinal ABCA4 transporter; abca4; ABCA4 |
UniProt ID | Q5F1L3 |
Protein Refseq | The length of the protein is 2363 amino acids long. The sequence is show below: MRFSAKVKLLLWKNWTLRKRQKLRLFVELVWPLSLFIILVWLRNANPLYGQHECHFPNKAMPSAGLLPWLQGIFCNTNNPCFKSPTRGESPGVVSNYNNSILSRAYSDAQELLLEKPEIHHLSRMWKELYAMSNLMDTLRTNPGKVSGRGIRVKDILKDDEILTLFLLKDIGLSDSVVYQLINAQIRVEQFAYGVPDLTLKDIACSQTLLERFIIFSSRRGMQTVRNSMCVLSQQRLQRIEDVLYASIDFFKLFEILPTVIDSSSRGIDLRFWGKVMSNLSDSIRELVQKPSIQDLLWVLRPLVQDGGPTTFTQLMNSLSDLFCGYPEGGGARVFSFNWYEDNNYKVFLGVNSTKKESYYLYDKTTTPFCNALIQSMESNPATKIAWSAMKPLLMGKVLFSPDSPAVREILKKANSTFEQLERVRQIGKSWEEVGPQLWNFLHNSVQMNIVRDTIKNPTVKEFLTRQLGDEGLTADDIINFLYNGNPDERPEGQVNYDWRNAFNITDHAVHLFNQYMECLTLDKFEGHDDESHLTHHALYLLEENKFWAGLVFLDMFPWTNNIPSHVKYKIRMDIDAVEKTNKIKDRYWDPGPRADPIEDMRYIWGGFAYLQDMIDHGIIKSQTSTEVPAGIYLQQMPYPCFVDDVFMITLNRCFPIFMVLAWIYSVSMLVKDIVLEKELRLKETMKNMGVTNDVIWLTWFIDSFTVMTTGTFLLTFVIVVGGVLHYSNPLILFCFLMAFTLATIMQAFLMSVFFSKANLAAACSGVIYFTLYLPHILCFAWQDRMTIKLKTLASFLSPVAFGFGTEYVSRYEEQGIGLQWGNIRQSPLEGDQYSFLFSIFMMLLDSLIYWTLAWYIDHVFPGEYGIPKPWYFPFLATYWCKFDHELVADGDSVQTELSIHEHVEENHIEPTDRQPEALSDGVKEEAEKSVKHEDLTVNKDSSSCKHKVKKEKEQEEKQKKDEQEKERNDKDEMNDSETNTGNPFYEPEPPGMVPGVCIQDLVKVYENTYKPAVDRMNITFYEGQITAFLGHNGAGKTTTLSIITGLFPPTSGTVWIRGRDIQTHMDSIRQSLGMCPQHNVLFRHLTVEEHILFYAQLKGKSKKQAERQVEVMLEDIGIPHKRNEEAQNLSGGMQRKLSVAMAFVGESKVVVLDEPTSGVDPYSRRSIWDLLLKYRSGRTIILSTHHMDEADLLGDRIAIISQGNSFAGGSPLFLKNCFGTGFYLTLVRRMRSIKDTGKKDSASCRSDCSCPCASCTPKAKEDPLEQELDGDISGLTELIHHHVPEAKLIESIGQELIYLLPSKDFKFRAYASLFRELEETLGDLGLSSFGISDTPLEEIFLKVTAESVTGTETPEEWMLQQRKSRTSLGVDNQTTVINIDNKGQESSIRKDTHHCVADKNPPNINEPPQGKKQNGKGSRQIKGTELLQQQFNALIIKRFKHATRSHKDFFAQIVLPASFVLLALVFTLIVPPFGEYPSLTLHPWIYGQQFVFFSNEHPGNEQMATFSNAFLNSPGLGTRCMKDQPLTKKFPCANTSNEWTMPVVSPSVTNILLSQEWTRDNPSPSCTCSTRSKLMMLPECPEGAGGRPPPQRIQPSSEIIQDLTERNVSDFLLKTYPDLIRSSMKSKYWVNEQRYGGISVGGKLPVLHVKEGDIISFFSHLGKMTNVTAGTTTKTVSQELQTFLQHLETEDNIKVWFNNKGWHSMVIFINVANNAILRANLGEDKDPEEYGITAMNHPLNLTKDQLSEVTVLTTSVDVVVAICVIFAMSFIPASFVLYLIQERVSNAKHLQFVSGVTPAIYWLTNFAWDIVNYALSVAMVVIIFFAFDKKAYTSSTNLPALIALLFFYGWAVIPMMYPASYLFNVPSTAYVALSCINLFIGINSSAITFILDLFENNRSLLKFNEKLKDLLLIFPHFCLGRGLIDLAMNQAVTDVYARFGEEHISNPFQWEFLGRNIFAMAVEGVVYFTLNLLIQHRFFLGTWFAEPPKGSIDGEDEDIAQERQRVMKGGGKNDILKLKELTKTYPGKQSPAVDRLCLGVRPGECFGLLGVNGAGKTTTFKMLTGDIQVTSGDASVAGYSILQDIADVHQNTGYCPQFDALDDLLTGREHLQLYGRLRGVPEDEIDMVADWGIEKLGVGKYADNLAGTYSGGNKRKLATAIALIGCPPVVLLDEPTTGMDPQSRRFLWNSIVSIIKEGRAVILTSHSMEECEALCTRLAIMVKGKFKCLGTIQHLKYKFGDGYIVTMKVRASKPGFAPDASPVEKFIQTNFPGSVQREKHYNMLQYQISSSSLARVFQLLISNKDSLNIEEYSVSQTTLDQVFVNFAKQQTDDEDIHLHPRAAGATRDVKVAPAPPPKTPAQ. |
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For Research Use Only | Not For Clinical Use.
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