Peroxisomal Biogenesis Factor 5
The product of this gene binds to the C-terminal PTS1-type tripeptide peroxisomal targeting signal (SKL-type) and plays an essential role in peroxisomal protein import. Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. The peroxisomal biogenesis disorders are a heterogeneous group with at least 14 complementation groups and with more than 1 phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause of neonatal adrenoleukodystrophy (NALD), a cause of Zellweger syndrome (ZWS) as well as may be a cause of infantile Refsum disease (IRD). Alternatively spliced transcript variants encoding different isoforms have been identified.
Mouse Anti-Yeast PEX5 Antibody (CBMOAB-02925CR) (CAT#: CBMOAB-02925CR)
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- Host species: Mouse
- Species Reactivity: Yeast
- Application: WB, ELISA
- Protein: Peroxisomal targeting signal receptor
- Size: 0.5mg, 1mg, 200µg
- Conjugate: Alexa Fluor 350, AP, APC, Biotin, Consult us more, Cy3, Cy5, Cy5.5, Cy7, FITC, HRP, NONE, PE, PerCP
- Alternative Names: Peroxisomal targeting signal receptor, PTS1 receptor, PTS1R, Peroxin-5, Peroxisomal protein PAS10, PEX5, PAS10, YDR244W
Mouse Anti-Arabidopsis PEX5 Antibody (CBMOAB-38663FYC) (CAT#: CBMOAB-38663FYC)
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- Host species: Mouse
- Species Reactivity: A. thaliana (Arabidopsis thaliana)
- Application: WB, ELISA
- Protein: Peroxisome biogenesis protein 5
- Size: 0.5mg, 1mg, 200µg
- Conjugate: Alexa Fluor 350, AP, APC, Biotin, Consult us more, Cy3, Cy5, Cy5.5, Cy7, FITC, HRP, None, PE, PerCP
- Alternative Names: Peroxisomal Biogenesis Factor 5, Peroxisome Receptor 1, Peroxisomal C-Terminal Targeting Signal Import Receptor, Peroxisomal Targeting Signal 1 Receptor, Peroxisomal Import Receptor 5, PTS1 Receptor, Peroxin-5, PTS1-BP, PTS1R
Mouse Anti-Rhesus PEX5 Antibody (CBMOAB-54306FYA) (CAT#: CBMOAB-54306FYA)
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- Host species: Mouse
- Species Reactivity: Rhesus (Macaca mulatta)
- Application: WB, ELISA
- Protein: PTS1-BP
- Size: 0.5mg, 1mg, 200µg
- Conjugate: Alexa Fluor 350, AP, APC, Biotin, Consult us more, Cy3, Cy5, Cy5.5, Cy7, FITC, HRP, NONE, PE, PerCP
- Alternative Names: PEX5
Mouse Anti-Rice PEX5 Antibody (CBMOAB-88572FYB) (CAT#: CBMOAB-88572FYB)
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- Host species: Mouse
- Species Reactivity: Rice (Oryza)
- Application: WB, ELISA
- Protein: Submitted name: Peroxisomal targeting signal 1 receptor long form
- Size: 0.5mg, 1mg, 200µg
- Conjugate: Alexa Fluor 350, AP, APC, Biotin, Consult us more, Cy3, Cy5, Cy5.5, Cy7, FITC, HRP, NONE, PE, PerCP
- Alternative Names: Peroxisomal targeting signal 1 receptor long form, PEX5
Mouse Anti-Rhesus PEX5 Antibody (MO-AB-05095W) (CAT#: MO-AB-05095W)
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- Host species: Mouse
- Species Reactivity: Rhesus (Macaca mulatta)
- Application: WB, ELISA
- Protein: PTS1-BP
- Size: 0.5mg, 1mg, 200µg
- Conjugate: Alexa Fluor 350, AP, APC, Biotin, Consult us more, Cy3, Cy5, Cy5.5, Cy7, FITC, HRP, NONE, PE, PerCP
- Alternative Names: Peroxisomal biogenesis factor 5 isoform d, PEX5
Mouse Anti-Chimpanzee PEX5 Antibody (MO-AB-12795W) (CAT#: MO-AB-12795W)
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- Host species: Mouse
- Species Reactivity: Chimpanzee (Pan troglodytes)
- Application: WB, ELISA
- Protein: PTS1-BP
- Size: 0.5mg, 1mg, 200µg
- Conjugate: Alexa Fluor 350, AP, APC, Biotin, Consult us more, Cy3, Cy5, Cy5.5, Cy7, FITC, HRP, NONE, PE, PerCP
- Alternative Names: Peroxisomal biogenesis factor 5, PEX5
Mouse Anti-Cattle PEX5 Antibody (MO-AB-17787R) (CAT#: MO-AB-17787R)
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- Host species: Mouse
- Species Reactivity: Cattle (Bos taurus)
- Application: WB, ELISA
- Protein: Peroxisomal targeting signal 1 receptor
- Size: 0.5mg, 1mg, 200µg
- Conjugate: Alexa Fluor 350, AP, APC, Biotin, Consult us more, Cy3, Cy5, Cy5.5, Cy7, FITC, HRP, NONE, PE, PerCP
- Alternative Names: Peroxisomal targeting signal 1 receptor, PTS1 receptor, PTS1R, PTS1-BP, Peroxin-5, Peroxisomal C-terminal targeting signal import receptor, Peroxisome receptor 1, PEX5, PXR1
Mouse Anti-Hamsters PEX5 Antibody (MO-AB-43352W) (CAT#: MO-AB-43352W)
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- Host species: Mouse
- Species Reactivity: Hamsters (Cricetinae)
- Application: WB, ELISA
- Protein: Peroxisomal targeting signal 1 receptor
- Size: 0.5mg, 1mg, 200µg
- Conjugate: Alexa Fluor 350, AP, APC, Biotin, Consult us more, Cy3, Cy5, Cy5.5, Cy7, FITC, HRP, NONE, PE, PerCP
- Alternative Names: Peroxisomal targeting signal 1 receptor, PTS1 receptor, PTS1R, PTS1-BP, Peroxin-5, Peroxisomal C-terminal targeting signal import receptor, Peroxisome receptor 1, PEX5
Mouse Anti-Marmoset PEX5 Antibody (MO-AB-61331W) (CAT#: MO-AB-61331W)
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- Host species: Mouse
- Species Reactivity: Marmoset
- Application: WB, ELISA
- Protein: PTS1-BP
- Size: 0.5mg, 1mg, 200µg
- Conjugate: Alexa Fluor 350, AP, APC, Biotin, Consult us more, Cy3, Cy5, Cy5.5, Cy7, FITC, HRP, NONE, PE, PerCP
- Alternative Names: Peroxisomal biogenesis factor 5 isoform d, PEX5
Rabbit Anti-PEX5 Antibody (MO-DKB-02810W) (CAT#: MO-DKB-02810W)
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- Host species: Rabbit
- Species Reactivity: A. thaliana (Arabidopsis thaliana)
- Application: WB
- Protein: Peroxisome biogenesis protein 5
- Size: 150µg
- Conjugate: NONE
- Alternative Names: Peroxisomal Biogenesis Factor 5, Peroxisome Receptor 1, Peroxisomal C-Terminal Targeting Signal Import Receptor, Peroxisomal Targeting Signal 1 Receptor, Peroxisomal Import Receptor 5, PTS1 Receptor, Peroxin-5, PTS1-BP, PTS1R, PEX5, ARABIDOPSIS PEROXIN 5, ATPEX5, EMB2790, EMBRYO DEFECTIVE 2790, PEROXIN 5
Mouse Anti-D. melanogaster Pex5 Antibody (CBMOAB-27484FYA) (CAT#: CBMOAB-27484FYA)
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- Host species: Mouse
- Species Reactivity: Fruit fly (Drosophila melanogaster)
- Application: WB, ELISA
- Protein: Submitted name: GH08708p
- Size: 0.5mg, 1mg, 200µg
- Conjugate: Alexa Fluor 350, AP, APC, Biotin, Consult us more, Cy3, Cy5, Cy5.5, Cy7, FITC, HRP, NONE, PE, PerCP
- Alternative Names: GH08708p, Peroxin 5, isoform A, Pex5, arm EG:63B12.5
Mouse Anti-Zebrafish pex5 Antibody (CBMOAB-92248FYA) (CAT#: CBMOAB-92248FYA)
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- Host species: Mouse
- Species Reactivity: Zebrafish (Danio rerio)
- Application: WB, ELISA
- Protein: PTS1-BP
- Size: 0.5mg, 1mg, 200µg
- Conjugate: Alexa Fluor 350, AP, APC, Biotin, Consult us more, Cy3, Cy5, Cy5.5, Cy7, FITC, HRP, NONE, PE, PerCP
- Alternative Names: pex5, Peroxisomal Biogenesis Factor 5