D-2-Hydroxyglutarate Dehydrogenase, Mitochondrial

This gene encodes D-2hydroxyglutarate dehydrogenase, a mitochondrial enzyme belonging to the FAD-binding oxidoreductase/transferase type 4 family. This enzyme, which is most active in liver and kidney but also active in heart and brain, converts D-2-hydroxyglutarate to 2-ketoglutarate. Mutations in this gene are present in D-2-hydroxyglutaric aciduria, a rare recessive neurometabolic disorder causing developmental delay, epilepsy, hypotonia, and dysmorphic features.D2HGDH (D-2-Hydroxyglutarate Dehydrogenase) is a Protein Coding gene. Diseases associated with D2HGDH include D-2-Hydroxyglutaric Aciduria 1 and 2-Hydroxyglutaric Aciduria. Among its related pathways are Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. and Pyruvate metabolism and Citric Acid (TCA) cycle. Gene Ontology (GO) annotations related to this gene include oxidoreductase activity and oxidoreductase activity, acting on CH-OH group of donors.Catalyzes the oxidation of D-2-hydroxyglutarate to alpha-ketoglutarate.

  • Mouse Anti-Rice D2HGDH Antibody (CBMOAB-22470FYB) (CAT#: CBMOAB-22470FYB)

    • Host species: Mouse
    • Species Reactivity: Rice (Oryza)
    • Application: WB, ELISA
    • Protein: Probable D-2-hydroxyglutarate dehydrogenase, mitochondrial
    • Size: 0.5mg, 1mg, 200µg
    • Conjugate: Alexa Fluor 350, AP, APC, Biotin, Consult us more, Cy3, Cy5, Cy5.5, Cy7, FITC, HRP, NONE, PE, PerCP
    • Alternative Names: Probable D-2-hydroxyglutarate dehydrogenase, mitochondrial, EC 1.1.99.39, D2HGDH, Os07g0187200 LOC_Os07g08950
  • Mouse Anti-Arabidopsis D2HGDH Antibody (CBMOAB-27341FYC) (CAT#: CBMOAB-27341FYC)

    • Host species: Mouse
    • Species Reactivity: A. thaliana (Arabidopsis thaliana)
    • Application: WB, ELISA
    • Protein: D-2-hydroxyglutarate dehydrogenase, mitochondrial
    • Size: 0.5mg, 1mg, 200µg
    • Conjugate: Alexa Fluor 350, AP, APC, Biotin, Consult us more, Cy3, Cy5, Cy5.5, Cy7, FITC, HRP, None, PE, PerCP
    • Alternative Names: D-2-Hydroxyglutarate Dehydrogenase, D2HGD, D-2-Hydroxyglutarate Dehydrogenase, Mitochondrial, EC 1.1.99.-, EC 1.1.99
  • Mouse Anti-Rhesus D2HGDH Antibody (CBMOAB-40357FYA) (CAT#: CBMOAB-40357FYA)

    • Host species: Mouse
    • Species Reactivity: Rhesus (Macaca mulatta)
    • Application: WB, ELISA
    • Protein: Submitted name: D-2-hydroxyglutarate dehydrogenase
    • Size: 0.5mg, 1mg, 200µg
    • Conjugate: Alexa Fluor 350, AP, APC, Biotin, Consult us more, Cy3, Cy5, Cy5.5, Cy7, FITC, HRP, NONE, PE, PerCP
    • Alternative Names: D2HGDH
  • Mouse Anti-Cattle D2HGDH Antibody (MO-AB-11161R) (CAT#: MO-AB-11161R)

    • Host species: Mouse
    • Species Reactivity: Cattle (Bos taurus)
    • Application: WB, ELISA
    • Protein: D-2-hydroxyglutarate dehydrogenase, mitochondrial
    • Size: 0.5mg, 1mg, 200µg
    • Conjugate: Alexa Fluor 350, AP, APC, Biotin, Consult us more, Cy3, Cy5, Cy5.5, Cy7, FITC, HRP, NONE, PE, PerCP
    • Alternative Names: D-2-hydroxyglutarate dehydrogenase, mitochondrial, EC 1.1.99.-, D2HGDH
  • Mouse Anti-Chimpanzee D2HGDH Antibody (MO-AB-20099W) (CAT#: MO-AB-20099W)

    • Host species: Mouse
    • Species Reactivity: Chimpanzee (Pan troglodytes)
    • Application: WB, ELISA
    • Protein: Submitted name: D-2-hydroxyglutarate dehydrogenase
    • Size: 0.5mg, 1mg, 200µg
    • Conjugate: Alexa Fluor 350, AP, APC, Biotin, Consult us more, Cy3, Cy5, Cy5.5, Cy7, FITC, HRP, NONE, PE, PerCP
    • Alternative Names: D-2-hydroxyglutarate dehydrogenase, D2HGDH
  • Mouse Anti-Marmoset D2HGDH Antibody (MO-AB-53876W) (CAT#: MO-AB-53876W)

    • Host species: Mouse
    • Species Reactivity: Marmoset
    • Application: WB, ELISA
    • Protein: Submitted name: D-2-hydroxyglutarate dehydrogenase, mitochondrial
    • Size: 0.5mg, 1mg, 200µg
    • Conjugate: Alexa Fluor 350, AP, APC, Biotin, Consult us more, Cy3, Cy5, Cy5.5, Cy7, FITC, HRP, NONE, PE, PerCP
    • Alternative Names: D-2-hydroxyglutarate dehydrogenase, mitochondrial, D2HGDH
  • Mouse Anti-Zebrafish d2hgdh Antibody (CBMOAB-72836FYA) (CAT#: CBMOAB-72836FYA)

    • Host species: Mouse
    • Species Reactivity: Zebrafish (Danio rerio)
    • Application: WB, ELISA
    • Protein: Submitted name: D-2-hydroxyglutarate dehydrogenase, mitochondrial
    • Size: 0.5mg, 1mg, 200µg
    • Conjugate: Alexa Fluor 350, AP, APC, Biotin, Consult us more, Cy3, Cy5, Cy5.5, Cy7, FITC, HRP, NONE, PE, PerCP
    • Alternative Names: D-2-hydroxyglutarate dehydrogenase, mitochondrial, d2hgd
  • Rabbit Anti-d2hgdh Antibody (MO-DKB-00206W) (CAT#: MO-DKB-00206W)

    • Host species: Rabbit
    • Species Reactivity: Zebrafish (Danio rerio)
    • Application: ELISA
    • Protein: D-2-hydroxyglutarate dehydrogenase, mitochondrial
    • Size: 0.1mg
    • Conjugate: Biotin, FITC, HRP, NONE
    • Alternative Names: D-2-hydroxyglutarate dehydrogenase, mitochondrial, EC 1.1.99.-, d2hgd
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